Alpha-synuclein aggregates trigger anti-viral immune pathways and RNA editing in human astrocytes

Output Details

Parkinson's disease is a neurodegenerative disease characterised by a proteinopathy with marked astrogliosis. To investigate how a proteinopathy may induce a reactive astrocyte state, and the consequence of reactive astrocytic states on neurons, we generated hiPSC-derived astrocytes, neurons and co-cultures and exposed them to small soluble alpha-synuclein aggregates. Oligomeric alpha-synuclein triggered an inflammatory state associated with TLR activation, viral responses, and cytokine secretion. This reactive state resulted in loss of neurosupportive functions, and the induction of neuronal toxicity. Notably, interferon response pathways were activated leading to upregulation, and isoform switching of the RNA deaminase enzyme, ADAR1. ADAR1 mediates A-to-I RNA editing, and increases in RNA editing were observed in inflammatory pathways in cells, as well as in post-mortem human PD brain. Aberrant, or dysregulated, ADAR1 responses and RNA editing may lead to sustained inflammatory reactive states in astrocytes triggered by alpha-synuclein aggregation, and this may drive the neuroinflammatory cascade in Parkinson's.
Tags
  • Alpha-synuclein
  • Astrocytes
  • Human
  • Immune response
  • Protein aggregates
  • RNA

Meet the Authors

  • User avatar fallback logo

    Karishma D’Sa, MSc

    Key Personnel: Team Wood Team Hardy

    University College London

  • Minee Choi, PhD

    Key Personnel: Team Wood

    The Francis Crick Institute

  • User avatar fallback logo

    Aaron Wagen, MD

    Key Personnel: Team Wood

    University College London

  • User avatar fallback logo

    Núria Setó-Salvia

  • User avatar fallback logo

    Olga Kopach

  • User avatar fallback logo

    James Evans, MSc

    Key Personnel: Team Wood

    University College London

  • User avatar fallback logo

    Margarida Rodrigues

  • User avatar fallback logo

    Patricia Lopez Garcia, PhD

    Key Personnel: Team Wood

    The Francis Crick Institute

  • User avatar fallback logo

    Ali Ghareeb

  • User avatar fallback logo

    James Bayne

  • Melissa Grant-Peters

    Key Personnel: Team Wood

    University College London

  • Sonia García-Ruiz, PhD

    Key Personnel: Team Hardy

    University College London

  • User avatar fallback logo

    Zhongbo Chen

  • User avatar fallback logo

    Samuel Rodriques

  • User avatar fallback logo

    Dilan Athauda

  • Emil Gustavsson, PhD

    Key Personnel: Team Wood Team Hardy

    University College London

  • User avatar fallback logo

    Sarah A Gagliano Taliun

  • User avatar fallback logo

    Regina H. Reynolds

  • User avatar fallback logo

    Goerge Young

  • User avatar fallback logo

    Stephanie Strohbuecker, PhD

    Key Personnel: Team Wood

    The Francis Crick Institute

  • User avatar fallback logo

    Tom Warner

  • User avatar fallback logo

    Dmitri A.Rusakov

  • User avatar fallback logo

    Rickie Patani

  • User avatar fallback logo

    Clare Bryant

  • User avatar fallback logo

    David Klenerman

  • Sonia Gandhi, PhD

    Co-PI (Core Leadership): Team Wood

    University College London

  • Mina Ryten

    Co-PI (Core Leadership): Team Hardy Team Wood

    University College London